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Rare, 100% fatal brain disease strikes 3 people in Oregon

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Three cases of a mad cow-like disease with a 100% fatality rate have been reported in a single county in Oregon .

Creutzfeldt-Jakob disease is a prion disease, meaning it's caused by abnormally folded proteins that damage brain tissue.

The disease is always fatal, with about 70% of those affected dying within a year of diagnosis.